Heterotaxy Syndrome with Intestinal Malrotation, Polysplenia and Azygos Continuity
نویسندگان
چکیده
منابع مشابه
Heterotaxy syndrome with intestinal malrotation, polysplenia and azygos continuity
Heterotaxy syndrome is a situs anomaly that comprises a large spectrum of cardiac and extracardiac malformations. Its association with intestinal malrotation is frequent. This later might be asymptomatic or manifest by signs of abdominal discomfort or of intestinal obstruction. We report on the case of a full term, small for gestational age neonate in whom heterotaxy syndrome with partial situs...
متن کاملAortic pseudocoarctation associated with polysplenia/heterotaxy syndrome.
Polysplenia/heterotaxy syndrome is a rare congenital disorder associated with a wide spectrum of anomalies in various organ systems. Although anomalies of the cardiovascular system are common in this syndrome, the authors report a rare case of polysplenia syndrome associated with aortic pseudocoarctation, which to our knowledge has never been reported.
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Polysplenia syndrome in association with situs inversus and intestinal atresia is rarely reported [1]. A 2-day-old male neonate was presented with neonatal intestinal obstruction. Abdominal radiograph showed air fluid levels suggestive of small bowel atresia. Ultrasound of the abdomen showed dilated bowel loops throughout the abdominal cavity. At operation, there was right sided stomach, centra...
متن کاملHeterotaxy syndrome and interrupted inferior vena cava (IVC) with azygos continuation
Heterotaxy syndrome or situs ambiguous is a rare congenital disease in which the pattern of anatomical organization of the thoraco-abdominal visceral and vascular structures is not arranged in normal position. Patients with heterotaxy syndrome represent a wide range of anatomical variations including thoraco-abdominal structures. Here we report a rare case of asymptomatic heterotaxy syndrome in...
متن کاملCase report of intestinal non-rotation, heterotaxy, and polysplenia in a patient with pancreatic cancer
RATIONALE Heterotaxy with polysplenia is an extremely rare congenital condition resulting from abnormal arrangement of organs in the abdominal and thoracic cavities during embryologic development. When a malignancy such as pancreatic cancer develops under these conditions, surgical resection becomes particularly complex. This case report demonstrates successful pancreatic cancer resection despi...
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ژورنال
عنوان ژورنال: Clinics and Practice
سال: 2018
ISSN: 2039-7283
DOI: 10.4081/cp.2018.1004